We present a case of an eleven-year-old boy presenting with progressive extrapyramidal signs and dementia.His imaging findings demonstrated the classic eye-of-the-tiger sign on T2W magnetic resonance imaging.He was Concealer diagnosed with pantothenate kinase-associated neurodegeneration (PKAN).This is a rare autosomal recessive Hats inborn error of coenzyme A metabolism, caused by mutations in PANK2.This is the first reported case of PKAN from the Caribbean.